Synovial sarcoma masquerading as thyroglossal cyst carcinoma

Authors

  • M. Babu Manohar Department of ENT, Apollo Main Hospital, Chennai, Tamil Nadu
  • P. S. J. Vikram Department of ENT, Apollo Main Hospital, Chennai, Tamil Nadu
  • R. Soorya Rao Department of ENT, Apollo Main Hospital, Chennai, Tamil Nadu

DOI:

https://doi.org/10.18203/issn.2454-5929.ijohns20184367

Keywords:

Synovial sarcoma, Monophasic, Thyroglossal cyst

Abstract

Synovial cell sarcoma is very rare in head and neck. It is usually seen in the extremities in close relation to the bursae and joints. In head and neck, most of the cases reported are in the retrohyoid, parapharyngeal and retropharyngeal areas. Reporting the case of a 18 year old man who presented with signs and symptoms of thyroglossal cyst. Radiological findings were suggestive of a haemorrhagic thyroglossal cyst or a cystic neoplasm. Frozen section revealed a malignant spindle cell neoplasm of mesenchymal origin. A Sistrunk operation was done. Histopathological and immunohistochemical analysis yielded a diagnosis of monophasic synovial sarcoma. Patient underwent intensity modulated radiotherapy according to tumor board decision. Follow up PET Scans were negative. We are reporting this case to highlight the rarity of the condition and the high index of suspicion required to diagnose such a synovial sarcoma in this area. Treatment should be aimed at complete surgical resection of the tumor and appropriate adjuvant radiotherapy.

Author Biographies

M. Babu Manohar, Department of ENT, Apollo Main Hospital, Chennai, Tamil Nadu

Consultant,Department of ENT
Apollo Main Hospitals, Greams Road, Chennai, Tamil Nadu

P. S. J. Vikram, Department of ENT, Apollo Main Hospital, Chennai, Tamil Nadu

Associate Consultant,Department of ENT
Apollo Main Hospitals, Greams Road, Chennai, Tamil Nadu

R. Soorya Rao, Department of ENT, Apollo Main Hospital, Chennai, Tamil Nadu

Registrar ,Department of ENT
Apollo Main Hospitals, Greams Road, Chennai, Tamil Nadu

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Published

2018-10-24